Search on: ARGININOSUCCINATE LYASE 
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Descriptor English:   Argininosuccinate Lyase 
Descriptor Spanish:   argininosuccinato liasa 
Descriptor Portuguese:   Argininossuccinato Liase 
Synonyms English:   Argininosuccinase
Lyase, Argininosuccinate  
Tree Number:   D08.811.520.232.300.400
Definition English:   An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease ARGININOSUCCINIC ACIDURIA in man. EC 4.3.2.1. 
Entry Combination - descr/qualif English:   Argininosuccinate Lyase/deficiency use Argininosuccinic Aciduria
 
See Related English:   Argininosuccinic Aciduria
 
History Note English:   1991(1975); use LYASES 1975-1990 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   1126 
Unique Identifier:   D001123 

Occurrence in VHL:
 

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